Celiac Disease

Brief Overview: Celiac Disease is an autoimmune condition. With Celiac Disease, when gluten is ingested, the body develops an immune response that attacks and damages the small intestine.

Prevalence: According to UpToDate, “The estimated global prevalence of celiac disease based on serologic studies is approximately 1 percent.”

Etiology: Typically, celiac disease has a genetic predisposition. Environmental factors are also thought to cause Celiac Disease. It is triggered by consuming gluten.

Risk Factors:

  • Family history of Celiac disease in first- and second-degree relatives
  • Type 1 Diabetes
  • Autoimmune thyroiditis
  • Down and Turner Syndromes
  • Pulmonary hemosiderosis
  • Several other autoimmune diseases also increase risk for Celiac Disease

Commonly Associated Conditions:

  • Selective IgA deficiency
  • Iron deficiency anemia
  • Osteoporosis
  • Type 1 Diabetes
  • Autoimmune thyroid disease, Hypothyroidism
  • Atopic dermatitis
  • GERD
  • Eosinophilic esophagitis
  • IBD – more frequently with ulcerative colitis than Crohn’s
  • Liver disease
  • Idiopathic pulmonary hemosiderosis
  • Cardiovascular disease – autoimmune myocarditis, idiopathic dilated cardiomyopathy
  • Kidney disease – Glomerular IgA deposition
  • Hyposplenism

Common Medications:

  • There is no medication for Celiac Disease. The treatment is to stop consuming gluten.
  • Corticosteroids may be used if there is severe inflammation that does not response to the gluten-free diet
  • Nutritional supplementation may be needed (like iron, Vitamin B12, Vitamin D, etc.)
  • Medications for symptoms, like diarrhea, or rash

Common Labs, Imaging, and Tests:

  • Serologic testing – tTG-IgA and total IgA, EMA-IgA
  • Upper endoscopy with small bowel biopsy
  • Vitamins A, D, E, B12, folic acid, ferritin, iron, prothrombin time. May also test for deficiencies in thiamine, B6, magnesium, copper, zinc, selenium

Common Symptoms:

  • Some people are asymptomatic
  • Abdominal pain
  • Diarrhea
  • Oily bowel movements that float
  • Weight loss
  • Bloated
  • Feeling full constantly
  • Poor appetite
  • Gas
  • Pruritic rash
  • Fatigue

Common Treatments:

  • Gluten-free diet
  • Management of any nutritional deficiencies

Physical Findings:

  • Abdominal tenderness, distention
  • Weight loss
  • Anemia
  • Dermatitis herpetiformis
  • Atrophic glossitis (oral lesions)

Potential Complications and Contraindications:

  • Constipation
  • Increased risk for lymphoma and GI cancer
  • Increased risk of microscopic colitis
  • Increased risk of pancreatitis
  • Nonresponsive celiac disease despite following a gluten-free diet
  • Refractory celiac disease
  • Ulcerative jejunitis
  • Skin conditions – dermatitis herpetiformis is the skin condition most commonly associated with celiac disease (this is itchy and burns, usually located in the lower back, buttocks, face, neck, trunk, knees, elbows)
  • Osteopenia
  • Medication absorption may be impacted

General Health and Lifestyle Guidance:

  • A DEXA scan may be recommended 12 months after starting a gluten-free diet
  • Calcium and vitamin D supplements may be recommended by your healthcare provider
  • Read food and medication labels carefully

Suggested Questions to Ask Patients:

  • Have you been diagnosed with celiac disease or have a family history of it?
  • Do you currently follow a gluten-free diet?
  • Have you experienced persistent GI symptoms, fatigue, or nutrient deficiencies?
  • Have you ever been tested for celiac antibodies or had a biopsy?
  • Are you working with a dietitian for meal planning?

Suggested Talking Points:

  • Work with your dietician to make sure you’re correctly following a gluten-free diet
  • Discuss the pneumonia vaccine with your healthcare provider
  • If you experience constipation, talk with your healthcare provider about fiber supplementation
  • Some people may need to use separate cooking utensils, toasters, microwaves, etc. from others living in the house to avoid cross-contamination with gluten-containing products

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